Imaging of Pulmonary Manifestations of Connective Tissue Diseases

Jitesh Ahuja, Deepika Arora, Jeffrey P. Kanne, Travis S. Henry, J. David Godwin

Research output: Contribution to journalReview articlepeer-review

35 Scopus citations

Abstract

Connective tissue diseases (CTDs) are a heterogeneous group of conditions characterized by circulating autoantibodies and autoimmune-mediated organ damage. Common CTDs with lung manifestations are rheumatoid arthritis, scleroderma or systemic sclerosis, Sjögren syndrome, polymyositis/dermatomyositis, systemic lupus erythematosis, mixed connective tissue disease, and undifferentiated connective tissue disease. The most common histopathologic patterns of CTD-related interstitial lung disease are nonspecific interstitial pneumonia, usual interstitial pneumonia, organizing pneumonia, and lymphoid interstitial pneumonia. Drug treatment of CTDs can cause complications, including opportunistic infection.

Original languageEnglish (US)
Pages (from-to)1015-1031
Number of pages17
JournalRadiologic Clinics of North America
Volume54
Issue number6
DOIs
StatePublished - Nov 1 2016
Externally publishedYes

Keywords

  • Autoimmune lung disease
  • Connective tissue disease
  • Interstitial lung disease

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging

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