Abstract
The term telangiectasia macularis eruptiva perstans (TMEP) was originally used to describe a rare form of cutaneous mastocytosis (CM) that was limited to the skin with lesions consisting of irregular, telangiectatic macules ranging in color from red to brown. Recent guidelines, however, recommended that the sole presence of telangiectasias should not form the basis of a distinct variant of CM. We conducted a review of the literature from 1930 to 2017 and found 76 cases that were reported as TMEP. Owing to a general misconception about diagnosis of CM and SM, there is a need for further discussion and awareness of the newly proposed World Health Organization (WHO) guidelines.
Original language | English (US) |
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Journal | Dermatology online journal |
Volume | 23 |
Issue number | 8 |
State | Published - 2017 |
Keywords
- AHN: systemic mastocytosis with associated hematologic neoplasm
- ASM: aggressive systemic mastocytosis
- CM: cutaneous mastocytosis
- DCM: diffuse cutaneous mastocytosis
- ISM: indolent SM
- MC: mast cells
- MCL: mast cell leukemia MCS: mast cell sarcoma
- MIS: mastocytosis in the skin
- MPCM: maculopapular cutaneous mastocytosis
- MPN: myeloproliferative neoplasms
- SM: systemic mastocytosis
- SSM: smoldering systemic mastocytosis
- TMEP: telangiectasia macularis eruptiva perstans
- UP: urticaria pigmentosa
- WHO: World Heatlh Organization
ASJC Scopus subject areas
- Dermatology