TY - CHAP
T1 - Unanticipated compression of the trachea in a 5-month-old undergoing an MRI for evaluation of neurofibromatosis
AU - Williams, Uduak Ursula
AU - Zavala, Aesa M.
AU - Van Meter, Antoinette
AU - Rebello, Elizabeth
AU - Tan, Jens
AU - Qwusu-Agyemang, Pascal
N1 - Publisher Copyright:
© 2016 International Anesthesia Research Society.
PY - 2018/1/1
Y1 - 2018/1/1
N2 - Neurofibromatosis type 1 is an autosomal-dominant disorder with the tendency toward the formation of tumors. Plexiform neurofibromas are the most common type of tumors seen in neurofibromatosis type 1. Approximately 50% oeeur in the head and neek region with a 5% ineidenee of airway involvement. We describe the ease of a 5 month old with a plexiform neurofibroma of the neek who developed complete airway obstruction on induction of anesthesia. Magnetic resonance imaging revealed a skull base neurofibroma extending to the hypopharynx and resulting in deviation of the airway. Because of the possibility of airway involvement, a eareful preanesthetic evaluation as well as a slow induction with the maintenance of spontaneous ventilation should be considered in patients presenting with facial neurofibromas.
AB - Neurofibromatosis type 1 is an autosomal-dominant disorder with the tendency toward the formation of tumors. Plexiform neurofibromas are the most common type of tumors seen in neurofibromatosis type 1. Approximately 50% oeeur in the head and neek region with a 5% ineidenee of airway involvement. We describe the ease of a 5 month old with a plexiform neurofibroma of the neek who developed complete airway obstruction on induction of anesthesia. Magnetic resonance imaging revealed a skull base neurofibroma extending to the hypopharynx and resulting in deviation of the airway. Because of the possibility of airway involvement, a eareful preanesthetic evaluation as well as a slow induction with the maintenance of spontaneous ventilation should be considered in patients presenting with facial neurofibromas.
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U2 - 10.1213/XAA.0000000000000407
DO - 10.1213/XAA.0000000000000407
M3 - Chapter
C2 - 28036318
AN - SCOPUS:85021850147
SN - 9781975115326
BT - 100 Selected Case Reports from Anesthesia and Analgesia
PB - Wolters Kluwer Health
ER -