Unusual Pancreatic Tumors

Pancreatic ductal adenocarcinoma and cystic neoplasms of the pancreas account for the majority of all pancreatic neoplasms. However, there is a subset of rare and unusual conditions of the pancreas that have been increasingly identified over the past two decades, in part by increased use of computed tomography. These conditions can often be challenging to clinicians because the presentation and diagnostic findings can often mimic pancreatic ductal adenocarcinoma. This chapter will focus on these less appreciated lesions and will discuss the optimal diagnostic and therapeutic approaches to their management.